BACKGROUND: Dyke-Davidoff-Masson syndrome (DDMS) is a
rare disease with unknown frequency, mainly presented with
seizures, facial asymmetry, contralateral hemiparesis and mental
retardation. Often, resulting from brain injury due to a multitude of
causes, especially in early life, associated with birth asphyxia.
Radiological findings include cerebral hemiatrophy/hypoplasia,
calvarial thickening, and hyperpneumatization of the frontal
sinuses.
CASE PRESENTATION: We report the case of a 17-year-old male
patient who presented to Neurology Clinic with complaints of left
side body weakness, walking difficulty and poorly controlled seizure
for the past 6 years. Brain MRI revealed atrophy of the right
cerebral hemisphere.
CONCLUSION: Dyke-Davidoff-Masson syndrome should be
suspected in any patients who present with classical features and
brain imaging showing hemiatrophy. Early identification and
treatment is important in such patients, as it can improve patients
prognosis and quality of life.
KEYWORDS: Dyke-Davidoff-Masson syndrome, Seizure, Cerebral
hemiatrophy,Magnetic resonance imaging

Published: 2019-05-28