Background: Lumbo-costo-vertebral syndrome is a set of rare abnormalities involving vertebral bodies, ribs, and abdominal wall.
Case: We present a case of Lumbo-costo-vertebral syndrome in a 6-month old female infant who had a progressive swelling over the right lumbar area since birth. Clinical examination revealed a reducible swelling on the right flank with positive cough impulse. Ultrasonography showed a defect containing bowel loops in the right lumbar region. Chest X-ray revealed scoliosis and hemi- vertebrae with absent lower ribs on the right side. Computer tomography scan showed hernia sac containing the bowel and the
right lobe of the liver with cross fused kidney.
Conclusion: Lumbo-costo-vertebraly syndrome is a rare condtion
which could be associated with different organ malformations. Simple closure or meshplasty could be done depending on the size of the defect.
KEYWORDS: lumbar hernia, lumbo-costo-vertebral, hemi- vertebrae